Recurrent LowGrade Fibromyxoid Sarcoma of the Nec

Authors: Aikaterini Mastoraki Theodoros Strigkos FotiosPanagiotis Tatakis Angela Christophi Vassilios Smyrniotis

Publish Date: 2015/06/30

Volume: 6, Issue: 3, Pages: 296-299

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Abstract

Lowgrade fibromyxoid sarcoma LGFMS represents a rare indolent benign neoplasm that proliferates at various anatomical locations Histologically the tumor consists of bland deceptively benignappearing spindle cells in a whirling pattern as well as myxoid and collagenized stroma The current treatment includes surgical excision The aim of this investigation was to analyze a rare clinical case of recurrent LGFMS of the neck Relevant literature is briefly reviewed An 81yearold male was admitted with an enlarging painless nontender mass in the neck The patient referred a past medical history of LGFMS Magnetic Resonance Imaging MRI depicted a large welldefined mass in the lower neck and supraclavicular area extending till the left upper area of the anterior thoracic wall Based on the imaging characteristics and the medical history a wide surgical excision of a 56 × 66 × 33 cm area in close proximity to the cervical vertebrae was performed On microsopic examination the tumor contained alternating fibrous and mixoid components with mixed hypo and hypercellular areas minimal necrosis and negligible cellular pleomorphism or nuclear atypia As LGFMS is a soft tissue malignancy any recurrences are usually local therefore treatment of choice is radical wide margin surgical excision Nevertheless the ideal goal of large safety margin of healthy tissue might be unattainable if it requires resection of vital anatomic structures Because LGFMS has a very low mitotic rate neither chemotherapy nor radiotherapy is expected to have significant effect on longterm prognosis

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