Authors: Shyamal Dasgupta Partha Mukhopadhyay Partha Pratim Sharma Nilufar Begum Aradhana Kalra
Publish Date: 2013/03/14
Volume: 62, Issue: 1, Pages: 83-84
Abstract
The Mayer–Rokitansky–Kuster–Hauser MRKH syndrome affects 1 out of 4500 women 1 It is a malformation of the female genitals due to interrupted embryonic development of the mullerian paramesonephric ducts in otherwise chromosomally phenotypically and endocrinologically normal female It is second to Turner’s syndrome as a cause of primary amenorrhea and was described by Mayer 1829 Rokitansky 1838 Kuster 1910 and Hauser and Schreiner 1961 in various literature studies which was later designated as MRKH syndrome MRKH syndrome is broadly subdivided into type A typical having symmetric uterine remnants and normal fallopian tubes and type B atypical with asymmetric uterine buds and abnormally developed fallopian tubes and other organ system anomalies
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