Authors: Elysa Widjaja Susan Blaser Charles Raybaud
Publish Date: 2006/04/21
Volume: 36, Issue: 6, Pages: 510-517
Abstract
Diffusion tensor imaging and tractography have been used to evaluate a variety of brain malformations However these studies have focused mainly on malformations involving the supratentorial compartments There is a paucity of data on diffusion tensor imaging of posterior fossa malformationsThe vermis was severely hypoplastic or absent in rhombencephalosynapsis and Joubert syndrome In rhombencephalosynapsis vertically oriented fibers were visualized in the midportion of the cerebellum The location of the deep cerebellar nuclei could be inferred from the amiculum and were medially located in rhombencephalosynapsis In the two patients with Joubert syndrome the horizontally arranged superior cerebellar peduncles were well demonstrated on the color vector maps Failure of the superior cerebellar peduncles to decussate in the mesencephalon was also well demonstrated on both color vector maps and tractography The deep cerebellar nuclei were more laterally located in Joubert syndrome
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