Authors: Alberto Mendoza Silvia Belda Rafael Salguero Miguel Angel Granados
Publish Date: 2010/05/22
Volume: 31, Issue: 6, Pages: 887-890
Abstract
The association of a complete atrioventricular block with long QT syndrome is relatively common and carries a high risk of torsades de pointes TdP and sudden death It is probably due to a downregulation of potassium channel currents I Ks and I Kr that impairs ventricular repolarization prolongs the QT interval and increases susceptibility to TdP so it must be considered a channelopathy This report describes a 6 yearold boy with a complete atrioventricular block diagnosed at 5 months of age who at the age of 1 year started having episodes of TdP associated with a prolonged QT interval He was treated successfully with propranolol and with a pacemaker implant At age 3 the complete atrioventricular block reversed spontaneously to a first degree atrioventricular block
Keywords: