Authors: B Stiller F Riedel K Paul F K H van Landeghem
Publish Date: 2014/05/01
Volume: 23, Issue: 1, Pages: 90-94
Abstract
We studied a 6yearold boy and a 2yearold girl with bronchitis fibroplastica following Fontan operation Large endobronchial casts of rubberlike consistency resulted in lifethreatening pulmonary failure In one patient symptoms improved after optimizing heart function with diuretics and in the other a dramatic improvement with the resolution of the clinical symptoms and normalized serum albumin followed subcutaneous highmolecularweight heparin treatment The severe relapse after discontinuation of the heparin medication and the once more successful treatment with heparin suggest that in addition to optimizing heart function highmolecularweight heparin might be a therapeutic option for this poorly understood condition
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