Authors: Nathalie WongChong Wondwossen Hailu Kidanewold Richard Kirsch Gary Robert May Judith Andrea McCart
Publish Date: 2011/10/18
Volume: 16, Issue: 3, Pages: 669-672
Abstract
Juvenile polyposis syndrome JPS is a rare autosomal dominant condition The polyps predominate in the colon but may be seen less commonly in the stomach or small intestine We report an unusual case of JPS associated with massive gastric polyposis resulting in a giant stomach severe anemia hematemesis proteinlosing enteropathy and gastric outlet obstruction Progressive complications ultimately necessitated a total gastrectomyA 27yearold woman presented in 2005 with severe anemia Gastroscopy revealed severe gastric polyposis Histopathology confirmed juvenile polyposis Gastrectomy was initially declined Progressive hematemesis hypoproteinemia and gastric outlet obstruction however resulted in a total gastrectomy 5 years following initial presentation Massive gastric polyposis resulted in severe gastromegaly
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